Cotyledonoid leiomyoma is a very rare tumor among the ever expanding repertoire of growth variants described in benign uterine leiomyoma. We report a case of cotyledonoid leiomyoma in a 39‑year‑old (unmarried) women presented with lump in abdomen. On laparotomy, a large multinodular, tan colored, exophytic, fungating tumor mass adherent to the posterolateral aspect of fundus of the uterus and extending to broad ligament and pelvic cavity was seen. Microscopic examination revealed nodules of smooth muscle cells arranged in fascicles with perinodular hydropic change diagnosed as cotyledonoid leiomyoma. We report it because of rarity and potential misinterpretation as a leiomyosarcoma.